Abstract
Phyllodes tumors of the vulva have an uncertain histogenetic origin. However, these tumors share morphological similarities with breast neoplasms. In view of its rarity, both the classification and the current treatment are not well established, with surgical resection being performed in most cases. We report the case of a 23-year-old Brazilian woman with a history of a vulvar mass in her left labia majora, whose transvaginal ultrasound revealed a nonspecific nodule with no vascularization on Doppler. The patient underwent exeresis of the lesion. The histological analysis was compatible with a benign phyllodes tumor of the vulva. When compared to the international literature, no cases have been reported among Brazilian women and this case is among the youngest affected by this condition. Although rare, phyllodes tumor should be remembered as a differential diagnosis for other vulvar tumors.
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